What is the Nakata index?

Nakata index is the sum of the cross-sectional area of the pulmonary arteries divided by the body surface area.

How to measure Nakata index?

The Nakata index was measured using the following formula: π × [right mid – main pulmonary artery diameter (mm)2 + left mid – main pulmonary artery diameter(mm)2]/[4 × BSA (m2)] (10).

What is overriding of aorta?

Definition. An overriding aorta is a congenital heart defect where the aorta is positioned directly over a ventricular septal defect, instead of over the left ventricle. The result is that the aorta receives some blood from the right ventricle, which reduces the amount of oxygen in the blood.

What does truncus arteriosus mean?

Truncus arteriosus is a birth defect of the heart. It occurs when the blood vessel coming out of the heart in the developing baby fails to separate completely during development, leaving a connection between the aorta and pulmonary artery.

How do you fix overriding aorta?

The ventricular septal defect is patched to stop the mixing of high-oxygen blood with low-oxygen blood between the ventricles. These repairs also fix the two remaining defects (overriding aorta and right ventricular hypertrophy).

Can truncus arteriosus be cured?

Truncus arteriosus must be treated through surgery. While your baby is waiting for surgery, he or she may need to take medications to reduce fluid in the lungs and have high-calorie feedings to build strength. Most babies with truncus arteriosus need surgery in the first few days or weeks of life.

What causes overriding aorta?

40,106 Overriding aorta is a result of the displacement of the outlet septum into the right ventricle, which causes the aortic root to be positioned directly over the VSD.

How do you get truncus arteriosus?

Is truncus arteriosus hereditary?

The exact cause of truncus arteriosus is not known. It has been suggested that some cases may develop due to the interaction of many genetic and environmental factors (multifactorial inheritance). The malformation is the result of an error in embryonic development.

What is the surgery for truncus arteriosus?

There are several procedures to correct truncus arteriosus. The most common procedure is called a Rastelli repair. The surgery involves: Using a patch to close the VSD, or hole in the heart.

What is a normal Nakata index for ecfo?

In 13 patients (22%) with a low Nakata index (under 200 mm 2 /m 2, lowest 125 mm 2 /m 2 ), the presence of a normal total lower lobe index (>90 mm 2 /m 2) enabled us to successfully perform ECFO combined with enlargement of the main pulmonary arteries in six of them [2].

Is the Nakata index more informative than the total lower lobe index?

We observed in our series that the total lower lobe index is more informative than the Nakata index for the selection of candidates for a Fontan operation.

Should we use LLI or Nakata index to evaluate adequacy?

We use LLI as being more predictive to evaluate adequacy of the pulmonary vascular tree, given that central pulmonary arteries used for calculation of Nakata index can be enlarged before or during a Fontan operation [4]. The lowest Nakata index that precludes a successful Fontan operation is not known [5].